Primary renal solitary fibrous tumour: case report and literature review
DOI: 10.22591/magyurol.2019.2.vrecenarl.69
Authors:
Vrecenár László dr.1, Galambos Csilla dr.2, Diczházi János Csaba dr.2, Buzogány István dr.1
1Péterfy Kórház-Rendelőintézet és Manninger Jenő Országos Traumatológiai Intézet, Urológiai osztály, Budapest (osztályvezető: Buzogány István dr.);
2Péterfy Kórház-Rendelőintézet és Manninger Jenő Országos Traumatológiai Intézet, Patológiai osztály, Budapest (osztályvezető: Diczházi János Csaba dr.)
Summary
Objective: The authors present a rare case of fibrotic tumour originating from the kidney and provide the literature review background.
Case report: The solitary fibrous tumour (SFT) is a rare mesenchymal neoplasm most frequently originating from the pleura. Renal occurrence is very uncommon. We report a 21-year-old male patient presenting with recurrent episodes of hypoglycaemia causing altered level of consciousness. Subsequent investigations revealed a tumour in the right kidney. The initial results of the core biopsy caused a diagnostic dilemma, but the immunohistochemical analysis of the radical nephrectomy specimen confirmed the primary renal solitary fibrous tumour. Our patient was doing well at the 3-month follow-up with no evidence of recurrence or metastasis.
Conclusion: The basis of its treatment is primarily surgical, which includes metastasectomy in metastatic cases. Considering the possibility of recurrence and distant metastasis formation, careful follow-up is recommended.